Re: Clinical case

From: Michael Brown (michael.brown@m.cc.utah.edu)
Date: Wed Jan 12 2000 - 13:45:53 EST


We have had experience with many pediatric cases regarding the distinction
of ALL from hematogones, and we continue to struggle with these interesting
and difficult cases.    We have not found any one particular marker that can
identify a cell as a lymphoid as opposed to a hematogone.  We find CD22
expression on normal immature and maturing B-cells as well, and use an
entire panel of B-cell markers in an attempt to assess maturation.
Maturational patterns of expression with CD10, CD20, CD22, CD24, TdT and
immunoglobulin light chains as well as CD45 can be useful.  Histograms of
ALL will usually exhibit fairly discreet, well-circumscribed populations
without evidence of maturation.  This guideline is not hard and fast,
however, and morphologic and clinical correlation is exceedingly important.
ALL patients usually have some symptomatology, such as malaise, fevers and
bone pain.

Acute lymphoblastic leukemia almost always presents with a rapid expansion
of lymphoid blasts and it would be very unusual for a patient to "smolder"
along with 12% blasts for 6 months, so if this patient has not been
diagnosed and treated for ALL, I strongly doubt that this presentation
represents that entity.  However, if the patient had a definitive diagnosis
and was treated, the situation gets very sticky.  We communicate closely
with the clinician, and err on the conservative side, as waiting another
week for the disease to declare itself is better than intensifying therapy.

Additionally, I'm not sure that the description of a "clonal" population is
accurate, as light chains restriction could not be demonstrated.  I have
been trained to limit the distinction of clonality to populations
demonstrate heavy or light chain restriction by flow cytometry or molecular
studies as well as T-cell gene receptor rearrangement by molecular studies.
I would appreciate comments from the community regarding this.

Michael S. Brown, MD
Hematopathology Fellow
Instructor
University of Utah
ARUP Laboratories, Inc.



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