Re: Clinical case

From: anpo@mb.ks.se
Date: Fri Jan 14 2000 - 05:34:52 EST


Hi,
I agree with you that the expression of individual markers is not relevant
and one has to look at patterns of B-cell maturation. The results from the
work of Concerted Action on Minimal Residual Disease has been published in
Leukemia, 1999,13,419-427 and I find these antibody combinations very
useful in clinical practice. In B-precursor ALL we find aberrant patterns
in at least one of combinations in approx. 90% of cases. In majority of
cases two or more combinations show aberrant patterns.
I also agree that in difficult cases the Ig and TCR rearrangement study
should be performed.
Best wishes
Anna

At 11:45 2000-01-12 -0700, you wrote:
>
>We have had experience with many pediatric cases regarding the distinction
>of ALL from hematogones, and we continue to struggle with these interesting
>and difficult cases.    We have not found any one particular marker that can
>identify a cell as a lymphoid as opposed to a hematogone.  We find CD22
>expression on normal immature and maturing B-cells as well, and use an
>entire panel of B-cell markers in an attempt to assess maturation.
>Maturational patterns of expression with CD10, CD20, CD22, CD24, TdT and
>immunoglobulin light chains as well as CD45 can be useful.  Histograms of
>ALL will usually exhibit fairly discreet, well-circumscribed populations
>without evidence of maturation.  This guideline is not hard and fast,
>however, and morphologic and clinical correlation is exceedingly important.
>ALL patients usually have some symptomatology, such as malaise, fevers and
>bone pain.
>
>Acute lymphoblastic leukemia almost always presents with a rapid expansion
>of lymphoid blasts and it would be very unusual for a patient to "smolder"
>along with 12% blasts for 6 months, so if this patient has not been
>diagnosed and treated for ALL, I strongly doubt that this presentation
>represents that entity.  However, if the patient had a definitive diagnosis
>and was treated, the situation gets very sticky.  We communicate closely
>with the clinician, and err on the conservative side, as waiting another
>week for the disease to declare itself is better than intensifying therapy.
>
>Additionally, I'm not sure that the description of a "clonal" population is
>accurate, as light chains restriction could not be demonstrated.  I have
>been trained to limit the distinction of clonality to populations
>demonstrate heavy or light chain restriction by flow cytometry or molecular
>studies as well as T-cell gene receptor rearrangement by molecular studies.
>I would appreciate comments from the community regarding this.
>
>Michael S. Brown, MD
>Hematopathology Fellow
>Instructor
>University of Utah
>ARUP Laboratories, Inc.
>
>
Anna Porwit
Haematopathology Lab.
Department of Pathology
Karolinska Hospital, Stockholm
anpo@mb.ks.se
tel.:+46-851774518
fax.:+46-851775843



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