Re: selective CD8 T cell deficit

From: Dr. Martin R. Hadam (Hadam.Martin@mh-hannover.de)
Date: Fri Mar 19 1999 - 07:42:38 EST


On Thu, 18 Mar 99 09:31:58 PST, Tom Mc Closkey wrote:

>Our division saw a patient yesterday with a n extremely low CD8 T 
>cell count (200 CD8s/ul), an 11 year old who has experienced recurrent 
>infections.  From the leterature I have found 2 defects which affect the 8s:
>comments are greatly appreciated.

 Over the years I've seen a number of such patients. Consistent finding
was the absence of bright CD8 cells, while dim CD8 / NK cells persist.
All except for one clinically presented as severe combined
immunodeficiencies. The single patient with exactly the same phenotype,
yet only marginally immunodeficient (if at all) was a girl then of ca 8
years.

 For a CD3gamma defect I'd anticipate lower levels of CD3 as well.


 Martin R. Hadam
 Kinderklinik - Medizinische Hochsch>ZAP70 results in complete absence of 8s and CD3 gamma defect which
>results also in absence of CD4 CD45RA cells (RA is normal), neither of
>which seem to fit.  Has anyone seen anthing like this?  Any thought s or
ule
 D-30623 Hannover
 Germany
 Email: Hadam.Martin@MH-Hannover.de



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